Malformações vasculares pulmonares congênitas: análise de 24 casos
Objective: To evaluate the casuistry of vascular malformations in our division and to analyze the predominant clinical findings of these malformations. Methods: A survey was carried out searching for all cases of pulmonary vascular malformations diagnosed, from August 1986 to December 2003. Through the analysis of the medical records of these patients, the following variables were evaluated: structural pulmonary alteration, clinical presentation, mean age at diagnosis, gender and clinical evolution. Results: The pathologies found were: pulmonary sequestration 6 cases (25%), agenesis and / or pulmonary hypoplasia 7 cases (30%), arteriovenous fistulas 4 cases (16%), vascular ring 6 cases (25%) and pulmonary valve agenesis 1 case (4%). Nine patients were male and 13 were female. Age at diagnosis ranged from 1 month to 58 years. The symptoms varied according to the pathology. The most frequent were recurrent respiratory infection, stridor, cyanosis, dyspnea. Of the 22 patients studied, 11 (50%) cases were amenable to surgical correction. Conclusion: Pulmonary vascular malformations are rare pathologies, but pediatricians should keep them in mind to obtain an early diagnosis, correct propaedeutics and, if possible, surgical correction of these pathologies.